Doty’s Method (Two sinus Reconstructions) of supravalvular Aortic stenosis in Williams’s syndrome

نویسندگان

  • Osman Tiryakioglu
  • Selma Kenar Tiryakioglu
  • Hasan Ari
  • Hakan Vural
  • Ahmet Ozyazicioglu
چکیده

We experienced a successful surgical Williams’s syndrome case of extended aortoplasty by means of Doty’s method (two sinus reconstructions) for congenital supravalvular aortic stenosis. Case was 29-year-old woman, who had no complaint except heart murmur and dyspnea. The retrograde aortography and Digital Subtraction Angiography (DSA) demonstrated localized stenosis just above the aortic valve, and it was an hour-glass type. This case showed excellent results. Doty’s aortoplasty was favorable method for supravalvular aortic stenosis without deformity of aortic valve and coronary obstruction.

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تاریخ انتشار 2009